VOCI DALLA STRADA: L'Alzheimer è stato passato ai pazienti dai cadaveri
L'Alzheimer è stato passato ai pazienti dai cadaveri
Cinque persone trattate con l'ormone della crescita umano contaminato hanno scoperto di aver sviluppato sintomi della malattia nonostante siano invecchiate da 38 a 55 anni Morbo di Alzheimer è stato passato a pazienti trattati con ormoni estratti da cadaveri, gli scienziati lo hanno dimostrato per la prima volta. Si ritiene che cinque persone abbiano sviluppato l'Alzheimer dopo essere state trattate con un ormone della crescita umano che conteneva inavvertitamente i semi della demenza. L'ormone contaminato è stato somministrato a oltre 1.800 bambini di bassa statura nel Regno Unito tra il 1959 e il 1995 prima di essere ritirato quando è stato dimostrato che si innesca Malattia di Creutzfeldt-Jakob (CJD).
Ora, gli scienziati dell'University College di Londra (UCL) hanno scoperto che lo stesso lotto responsabile dei casi di CJD sembra aver innescato l'Alzheimer in alcuni pazienti. Il più giovane ha sviluppato sintomi di demenza a soli 38 anni. Il professor John Collinge, direttore dell'UCL Institute of Prion Diseases e un neurologo consulente, autore principale della ricerca, ha dichiarato: “ Non stiamo suggerendo per un momento che puoi prendere la malattia di Alzheimer. Non puoi prenderlo essendo un assistente o vivendo con un marito o una moglie con la malattia.“Ai pazienti che abbiamo descritto è stato somministrato un trattamento medico specifico e a lungo termine che ha comportato l'iniezione di pazienti con materiale ora noto per essere stato contaminato con proteine correlate alla malattia. Tuttavia, il riconoscimento della trasmissione in queste rare situazioni dovrebbe portarci a rivedere le misure per prevenire trasmissione accidentale tramite altre procedure mediche o chirurgiche , al fine di prevenire tali casi in futuro” Proteine amiloidi-beta trovate nell'ormone Gli scienziati britannici inizialmente si imbatterono nella scoperta mentre studiavano il cervello di otto persone che morirono di CJD dopo essere state iniettate con un ormone della crescita umano.
Inaspettatamente, quattro dei pazienti presentavano livelli enormi di proteina beta amiloide, un deposito appiccicoso che si forma tra le cellule cerebrali e impedisce loro di comunicare correttamente tra loro.
Sebbene nessuno di loro avesse sviluppato la demenza, secondo gli scienziati è probabile che l'avrebbero fatto se fossero vissuti più a lungo.
I ricercatori hanno quindi rintracciato l'ormone della crescita originale, conservato dal Ministero della Salute, e hanno scoperto che conteneva le proteine amiloidi-beta mal ripiegate implicate nell'Alzheimer.
Iniettando l'ormone vietato nel cervello dei topi, gli animali hanno iniziato a sviluppare i segni della malattia neurodegenerativa.
Gli scienziati hanno scoperto che cinque persone trattate con l'ormone hanno sviluppato i sintomi del morbo di Alzheimer nonostante avessero un'età compresa tra i 38 e i 55 anni. Nessuna era a rischio genetico per la malattia.
Il primo autore, il dottor Gargi Banerjee, dell'UCL Institute of Prion Diseases, ha dichiarato: "Abbiamo scoperto che è possibile trasmettere la patologia dell'amiloide-beta e contribuire allo sviluppo del morbo di Alzheimer".
"Questa trasmissione si è verificata in seguito al trattamento con una forma ormai obsoleta di ormone della crescita e ha comportato trattamenti ripetuti con materiale contaminato, spesso per diversi anni. Non ci sono indicazioni che la malattia di Alzheimer possa essere acquisita da un contatto ravvicinato o durante l'erogazione di cure di routine". Le proteine amiloidi si presentano in diversi ceppi
Si ritiene che le proteine amiloidi mal ripiegate si raggruppino in "pile" che crescono nel tempo fino a diventare così lunghe da spezzarsi, creando nuovi "semi".
Ogni seme continua a crescere, finché l'accumulo incontrollato di amiloide nel cervello inizia a uccidere le cellule cerebrali.
La dottoressa Susan Kohlhaas, direttore esecutivo della ricerca e delle partnership di Alzheimer's Research UK, ha dichiarato: "Questo studio ha rivelato di più su come i frammenti di amiloide possono diffondersi all'interno del cervello, fornendo ulteriori indizi su come la malattia di Alzheimer progredisce e potenziali nuovi bersagli per i trattamenti di domani".
Non sono stati segnalati casi di Alzheimer acquisiti a seguito di altre procedure mediche o chirurgiche, ma gli esperti hanno affermato che è importante rivedere le misure ed eventualmente introdurre metodi di decontaminazione migliori per le attrezzature chirurgiche.
Il team ha anche scoperto che le proteine amiloidi si presentano in ceppi diversi, come i virus, e che i farmaci che colpiscono il ceppo principale potrebbero consentire lo sviluppo di forme meno dominanti, che non sono curabili.
Il coautore, il professor Jonathan Schott, consulente neurologo onorario dell'UCL, ha dichiarato: "Questi risultati forniscono intuizioni potenzialmente preziose sui meccanismi della malattia e aprono la strada a ulteriori ricerche che speriamo possano approfondire la comprensione delle cause della malattia di Alzheimer più tipica e a insorgenza tardiva". Commentando la nuova ricerca, il dottor Richard Oakley, direttore associato per la ricerca e l'innovazione dell'Alzheimer's Society, ha dichiarato:
"Non è noto quanto fosse comune la trasmissione dell'Alzheimer nelle 1.800 persone sottoposte a questo trattamento e lo studio ha preso in esame solo le cartelle cliniche di otto persone.
Oggi i pazienti ricevono alternative sintetiche che sono state approvate per la sicurezza e non presentano rischi di trasmissione di malattie".
La ricerca è stata pubblicata sulla rivista Nature Medicine.
Fonte: https://www.telegraph.co.uk/news/2024/01/29/alzheimers-passed-on-medical-donors-ucl-study/
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yieldlab.net, 2172218, RESELLER
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# END ads.txt - vocidallastrada.org - 2023-10-18 14:39:45
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